Excess of Pappenheimer Bodies (Siderocytes) in Two Splenectomized Siblings with Congenital Dyserythropoietic Anemia – Type II (CDA-II) and Iron Overload
Ladislav Chrobák,
Jindřiška Matysová
Affiliations
Ladislav Chrobák
Charles University in Prague, Faculty of Medicine and University Hospital in Hradec Králové, 2nd Department of Medicine, Division of Clinical Hematology, Hradec Králové, Czech Republic
Jindřiška Matysová
Charles University in Prague, Faculty of Medicine and University Hospital in Hradec Králové, 2nd Department of Medicine, Division of Clinical Hematology, Hradec Králové, Czech Republic
In two splenectomized siblings with congenital dyserythropoietic anemia type –II (CDA-II) and iron overload excess of Pappenheimer bodies reaching 46.4 % and 15.9 % respectively was found. Cause, significance and differential diagnosis of this finding were discussed.