Journal of Pediatric Surgery Case Reports (May 2023)

Dermatofibrosarcoma protuberans case report: Aggressive tumor in a preadolescent child

  • Andres F. Espinoza,
  • Ekene Onwuka,
  • M John Hicks,
  • Prakash Masand,
  • Laura Monson,
  • M. Fatih Okcu,
  • Nina Pinglay,
  • Allison Vidimos,
  • Sanjeev A. Vasudevan

Journal volume & issue
Vol. 92
p. 102612

Abstract

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Dermatofibrosarcoma Protuberans is an aggressive form of skin cancer in children. It has a slow growth rate and low chance of metastasizing but is notorious for its aggressive invasive and recurrent nature. In pediatric patients, the resections can be quite aggressive but with appropriate surgical planning and approach, can have quite low morbidity and mortality. We report a unique case of a pediatric patient with dermatofibrosarcoma protuberans that was managed with repeated surgical resections, discuss operative management strategies for this aggressive diagnosis, and provide a review of the literature.

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