Autopsy and Case Reports (Sep 2011)

Fatal pulmonary thromboembolism associated with hemoglobin SC disease in a 15 year-old boy

  • Thiago Trolez Amancio,
  • Anderson da Costa Lino Costa,
  • Marcela Longo Borsato,
  • Leandro Marins,
  • Lívia Moscardi Bacchi,
  • Maria Claudia Nogueira Zerbini

DOI
https://doi.org/10.4322/acr.%y.26063
Journal volume & issue
Vol. 1, no. 3

Abstract

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We report a case of hemoglobin SC disease complicated by fatal pulmonary thromboembolism in a 15 year-old Brazilian boy, submitted to autopsy. This case shows the importance of early diagnosis and treatment of sickle cell disease, which generates systemic involvement in youth and the importance of considering the hypercoagulability in these patients. The autopsy was very instructive, revealing the florid morphologic aspect of sickle cell disease and its complications.

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