Giant Encephalocele

Abstract

Giant Encephalocele is a rare entity in which the central nervous system structures in any combination protrude through a defect in the skull and the size of the head is smaller than that of the deformity. A few cases are reported globally. It could be existed alone or in combination with other central nervous system (CNS) anomalies. We report a case of 4 months old child with giant encephalocele associated with hand deformity. She underwent excision of the sac and the patient is doing well after 3 months follow up.

Keywords

• Giant encephalocele
• Deformity
• Excision
• Central nervous system