Sultan Qaboos University Medical Journal (Nov 2013)

Sporadic Lateral Ventricular Hemangioblastoma presenting with Intraventricular and Subarachnoid Haemorrhage

  • Mahasen Al-Najar,
  • Azmy Al-Hadidy,
  • Alaa Saleh,
  • Ahmad Al-Tamimi,
  • Asaad Al-Darawish,
  • Fatima Obeidat

Journal volume & issue
Vol. 13, no. 4
pp. 597 – 600

Abstract

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Intraventricular hemangioblastoma (HB) is very rare; few cases of intraventricular HB have been reported in the literature, either sporadically or in association with von Hippel-Lindau disease. Furthermore, the incidence of ventricular haemorrhage from HB seems to be uncommon. We report a unique case of sporadic HB of the right lateral ventricle presenting with intratumoural and intraventricular haemorrhage in addition to multifocal intracranial superficial siderosis, indicating the presence of a subarachnoid haemorrhage (SAH) as well. Such a combination has not been reported before. In the future, the detection of an intraventricular mass in association with ventricular haemorrhage, with or without SAH, should include HB as a differential diagnosis, particularly when the imaging appearances are not typical of the more common intraventricular tumours.

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