Extranodal Rosai-Dorfman Disease Presenting as a Pericardial Mass and Constrictive Pericarditis

Chirag K. Desai, MD; Sharonne N. Hayes, MD; Mithun Vinod Shah, MD, PhD; Joseph J. Maleszewski, MD; Jonathan Bleeker, MD; Kelly Steffen, DO; Maria Stys, MD

JACC: Case Reports (Dec 2019)

Extranodal Rosai-Dorfman Disease Presenting as a Pericardial Mass and Constrictive Pericarditis

Chirag K. Desai, MD,
Sharonne N. Hayes, MD,
Mithun Vinod Shah, MD, PhD,
Joseph J. Maleszewski, MD,
Jonathan Bleeker, MD,
Kelly Steffen, DO,
Maria Stys, MD

Affiliations

Chirag K. Desai, MD: Division of Cardiovascular Disease, University of South Dakota Sanford School of Medicine, Sioux Falls, South Dakota; Address for correspondence: Dr. Chirag K. Desai, Division of Cardiovascular Disease, University of South Dakota Sanford School of Medicine, 1306 West 18th Street, Sioux Falls, South Dakota 57106.
Sharonne N. Hayes, MD: Department of Cardiovascular Medicine, Mayo Clinic, Rochester, Minnesota
Mithun Vinod Shah, MD, PhD: Division of Hematology, Mayo Clinic, Rochester, Minnesota
Joseph J. Maleszewski, MD: Department of Cardiovascular Medicine, Mayo Clinic, Rochester, Minnesota; Department of Laboratory Medicine and Pathology, Mayo Clinic, Rochester, Minnesota
Jonathan Bleeker, MD: Department of Internal Medicine, University of South Dakota Sanford School of Medicine, Sioux Falls, South Dakota
Kelly Steffen, DO: Division of Cardiovascular Disease, University of South Dakota Sanford School of Medicine, Sioux Falls, South Dakota
Maria Stys, MD: Division of Cardiovascular Disease, University of South Dakota Sanford School of Medicine, Sioux Falls, South Dakota

Journal volume & issue: Vol. 1, no. 4
pp. 643 – 647

Abstract

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Rosai-Dorfman disease is a rare, idiopathic disorder of histiocyte proliferation. We describe a case of a 59-year-old woman who presented with heart failure symptoms from a large pericardial mass causing constrictive pericarditis. Pathologic findings including immunohistochemistry suggested the diagnosis. She was treated with corticosteroids and improved clinically. (Level of Difficulty: Advanced.)

Published in JACC: Case Reports

ISSN: 2666-0849 (Online)
Publisher: Elsevier
Country of publisher: United States
LCC subjects: Medicine: Internal medicine: Specialties of internal medicine: Diseases of the circulatory (Cardiovascular) system
Website: https://www.journals.elsevier.com/jacc-case-reports

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Abstract

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