Congenital intrahepatic portosystemic shunts: Imaging findings and endovascular management

Abstract

We present two cases of congenital intrahepatic portosystemic shunts in which the right portal vein directly communicated with the inferior venacava (IVC) in one patient and with the hepatic vein in the other. Multiple hepatic nodules consistent with focal nodular hyperplasia (FNH) were seen in the first patient. The second patient presented with recurrent history of hepatic encephalopathy. Percutaneous transhepatic embolization was performed using coils and Amplatz device following which she completely recovered.

Keywords

• amplatzer device
• amplatz vascular occluder device
• congenital portosystemic shunts
• hepatic encephalopathy
• hypertrophied hepatic artery
• intrahepatic portosystemic shunts
• portal vein hypoplasias