Congenital stapes fixation with uncommon middle ear defects: a case report

Abstract

The presence of congenital stapes footplate fixation with other congenital ossicular defects or middle ear anomalies is a rare condition. Anomaly can be sporadic or a part of a syndrome originated from first or second branchial arch. Here we report a case of 10 years old female patient who appealed to our clinic with the complaint of non-progressive hearing loss from 2 years of age at her left ear. When an exploratory tympanotomy was performed, stapes footplate fixation with absent stapedial tendon and defective long process of incus was the pathology. When literature was evaluated, it was realized that this is a unique case who has these kinds of multiple abnormalities at the same time.

Keywords

• congenital
• middle ear anomaly
• stapedial tendon
• stapes footplate fixation
• incus defect