World Journal of Surgical Oncology (Mar 2006)

Desmoid tumor in Gardner's Syndrome presented as acute abdomen

  • Rizos Spiros,
  • Filippou Georgios,
  • Papadopoulos Vasilios,
  • Filippou Dimitrios,
  • Hatzimarkou Andreas,
  • Skandalakis Panagiotis

DOI
https://doi.org/10.1186/1477-7819-4-18
Journal volume & issue
Vol. 4, no. 1
p. 18

Abstract

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Abstract Background Gardner's syndrome can occasionally be complicated with intra-abdominal desmoid tumor. These tumors usually remain asymptomatic but can exhibit symptoms due to intestinal, vascular and ureteral compression and obstruction. Case presentation A rare case of a 41-year-old male patient with Gardner's syndrome complicated with intra-abdominal desmoid tumor, which first presented as acute abdomen, is presented. Conclusion Extra-abdominal manifestations of Gardner's syndrome along with a palpable abdominal mass would raise suspicion for the presence of a desmoid tumor in the majority of cases. In life-threatening cases, surgical treatment should be considered as a palliative approach, though the extent of excision remains debatable