Multidisciplinary management of adult cloacal exstrophy complications: A challenging case of nephrolithiasis and abdominal wall extrusion of a catheterizable ileal pouch

Abstract

Cloacal exstrophy is a rare congenital syndrome which comprises multiple genitourinary, gastrointestinal and musculoskeletal anomalies. The long-term effects following childhood cloacal exstrophy management is poorly characterized in living adults. In this report, a 42-year-old female born with cloacal exstrophy presented after numerous prior surgical reconstructions with abdominal extrusion of a catheterizable ileal pouch and bilateral staghorn calculi. We review the steps in surgical management of this uncommon scenario with a goal of improving the patient's quality of life.

Keywords

• Cloacal exstrophy
• Urinary diversion
• Fecal diversion
• Abdominal wall reconstruction
• Multidisciplinary surgery