Duplication of Superior Vena Cava with Atrial Termination of Right Hepatic Vein in Tetralogy of Fallot: A Rare Association

Abstract

Anomalous hepatic venous drainage into the right atrium in association with Tetralogy of Fallot (TOF) is a rare presentation. Here, authors present a very interesting case of anomalous hepatic venous drainage into the right atrium. A 23-year-old patient presented with vascular combination of duplication of Superior Vena Cava (SVC) with an atrial termination of Right Hepatic Vein (RHV) in TOF. Separate cannulation and looping were required to have a better venous drainage while performing the intracardiac procedures through right atrium on cardiopulmonary bypass. This was the first case of this kind reported in the literature.

Keywords

• cyanosis
• hepatic venous drainage
• persistent left sided superior vena cava