Journal of Indian Association of Pediatric Surgeons (Jan 2017)

Primary pulmonary rhabdomyosarcoma in a child

  • Raghunandan Balaji,
  • Prasanna Kumar,
  • Isha Garg,
  • Kanishka Das

DOI
https://doi.org/10.4103/0971-9261.194629
Journal volume & issue
Vol. 22, no. 1
pp. 57 – 59

Abstract

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A 9-year-old female presented with fever, cough, and hemoptysis for a week. The chest skiagram and contrast-enhanced computerized tomography delineated a well-defined solid lesion localized to the superior segment of the right lower lobe with features of a congenital pulmonary airway malformation. The lesion was surgically managed with a segmentectomy and histopathology confirmed a contained pulmonary rhabdomyosarcoma (RMS). No other primary site of origin was evident, and a final diagnosis of "primary" pulmonary RMS was made. She received adjuvant chemotherapy and was disease free after 6 years of surveillance. The unique clinicoradiological features of the case are discussed and the sparse literature is reviewed.

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