Pulmonary haemangiolymphangioma as cause of hemodynamic decompensation

Abstract

Introduction: Vascular malformations are anomalies caused by errors in the embryonic differentiation including a large number of diseases of the venous and lymphatic capillary network. They are rare (0.05–3%), and are classified according to their basic structural components (capillary, venous, lymphatic, arterial and combined forms) Case description: Three-months-old boy, was admitted with respiratory distress; and medical history of bronchopulmonary dysplasia and chronic malnutrition, both treated with unknown manage. During the physical examination he was found: with poor general condition, atrial murmur grade IV and bilateral crackles on auscultation. Anteroposterior and lateral radiographs of the chest were taken; which they revealed polyhedral images in mediastinum and right chest; as well as cardiac silhouette shifted. It was performed chest CT; in where multiple intrapulmonary air cysts in the middle lobe were observed; just as in previous and basal segments of the lower lobe of the right lung lesions rounded morphology. It was made right middle lobectomy. Pathologic findings reported cellular elements compatible with hemangio-lymphangioma. Conclusion: Despite its “benign” histological quality, the hemangiolynphangioms are relate to severe deformity of cavity and limbs, due to the high capacity to invade locally organs and adjacent tissues (muscle, bone and soft tissue), accompanied by growth fast and high probability of local recurrence. Therefore, generally associated symptoms are mainly mechanical nature and depend on the damage to adjacent tissue, anatomic location of the lesion and the same size.

Keywords

• Hemangiolymphangioma
• Vascular malformation
• Lymphatic malformation