Radiology Case Reports (Jun 2021)

A rare case of inflammatory myofibroblastic tumor of the vulva in a newborn

  • Bui-Van Lenh, MD, PhD,
  • Nguyen Minh Duc, MD, M.Sc,
  • Thieu-Thi Tra My, MD,
  • Nguyen Dinh Van, MD,
  • Bui-Thi My Huong, MD,
  • Hoang-Van Trung, MD,
  • Mai Tan Lien Bang, MD,
  • Pham Minh Thong, MD, PhD

Journal volume & issue
Vol. 16, no. 6
pp. 1352 – 1354

Abstract

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Inflammatory myofibroblastic tumor (IMT) is an uncommon neoplasm that rarely arises in the genitourinary system. IMTs in the vulva in infants are extremely rare in the literature. The tumor consists of myofibroblastic spindle cells accompanied by inflammatory cell infiltration. In this article, we aimed to describe the case of IMT in the vulva. A newborn girl presented with a mass in the vulva detected in the prenatal period. The patient was treated with surgery and chemotherapy. Follow-up 8 months after surgery showed no signs of recurrence. In conclusion, IMT has a variable clinical presentation, surgery is the optimal approach, but in cases without complete resection, chemotherapy is essential.

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