Splenic Kasabach-Merritt syndrome in an adult. Presentation of a case and review of the topic

Abstract

A 22-year-old male black patient presented with big splenomegaly due to a giant hemangioma of the spleen, showing thrombocytopenia and bleeding disorders. A Kasabach-Merrit syndrome was diagnosed. An anterior total splenectomy was performed, returning the platelet count and coagulation disorders back to normal. His evolution was favorable after 18 months of follow-up. Splenectomy surgical treatment was recommended. The topic was reviewed due to the infrequency of the disease.

Keywords

• kasabach-merritt
• esplenomegalia
• hemangioma esplénico
• trombocitopenia
• coagulopatía de consumo