Pulmonary lymphangioleiomyomatosis (case report)

Abstract

This article presents a clinical observation of a patient with a proven diffuse-nodular form of lymphangioleiomyomatosis of the lungs. Features of the course of the process against the background of pathogenetic therapy which included sirolimus and progesterone have been considered. It is necessary to raise awareness of doctors about the disease that facilitates timely diagnosis and treatment.

Keywords

• anti-estrogen LAM therapy
• pulmonary lymphangioleiomyomatosis (LAM)