Gradenigo's syndrome as a first manifestation of rhabdomyosarcoma

Abstract

Introduction: Rhabdomyosarcoma is a malignant neoplasm with origin from voluntary muscles and causes approximately 50% of all tumors of soft part in children. The embryonal subtype is the most common in the head and neck region, its location in the middle ears and mastoid is uncommon and of the worst prognosis due to the high incidence of intracranial extension. the signs and symptoms depend on the location of the tumor. Objective: The objective of this case report was to carry out a brief review on the Rhabdomyosarcoma and Gradenigo's Syndrome association and clarify the importance of the differential diagnosis in this kind of pathology. Case Report: In this work we report the case of a five-year-old boy with diagnosis of temporal bone Rhabdomyosarcoma that presented with a case of Gradenigo's Syndrome (abducens paralysis, otorrhea/otalgia, retroorbitary pain) and facial nerve paralysis.

Keywords

• Gradenigo's syndrome
• Facial paralysis
• Temporal bone
• Rhabdomyosarcoma