Acropigmentation of DohiA Rare Presentation

Abstract

Reticulate Acropigmentation of Dohi or Dyschromatosis symmetrica hereditaria, is an autosomal dominant genodermatosis, with very few reported autosomal recessive traits mostly seen in the Japanese population. A 27-year-old Indian male presented with light and dark coloured lesions involving bilateral arms and forearms, chest, back, and bilateral lower limbs with sparing of face, palms, and soles from 20 years. There were multiple hyperpigmented and hypopigmented macules which on detailed cutaneous examination and biopsy was diagnosed as reticulate acropigmentation of Dohi. As no definitive and effective treatment is available in this condition, the patient was treated conservatively with sun protection and sunscreen to decrease the contrast between hyperpigmented and hypopigmented lesions however the patient could not be followed-up further. Acropigmentation of Dohi being a rare entity diagnosing and differentiating it from other disorders is important.

Keywords

• autosomal dominant
• autosomal recessive
• dyschromatosis symmetrica hereditaria
• dyschromatosis symmetrica universalis
• genodermatosis