Primary Ewing’s sarcoma of the right maxillary sinus in a young girl: A rare case report

Abstract

The Ewing sarcoma family of tumors (ESFT) stands for a group of rare and aggressive malignancies consisting of high grade poorly differentiated small round blue cells. In our case report, we aim to describe the clinical presentation, diagnosis and the treatment plan for our patient. A 16-year-old girl presented to the ENT outpatient department of the Mayo Hospital Lahore with the complaints of right nasal obstruction, epistaxis from right nose, swelling on the right cheek and headaches. Examination revealed a soft, tender swelling on her right cheek below the right eye. Imaging revealed a heterogeneous opacity in the right nose and right maxillary sinus with erosion of the sinus walls.Very few such cases have been reported in international literature. Being a rare case, our article will add insights to the literature regarding complex clinical presentation, diagnostic evaluation and treatment of the sinonasal Ewing sarcoma.

Keywords

• Ewing sarcoma
• paranasal sinuses
• neuroectodermal tumor
• epistaxis