Herlyn-Werner-Wunderlich syndrome: A rare cause of abdominal pain and dyspareunia

Abstract

Herlyn-Werner-Wunderlich (HWW) syndrome is a rare congenital disease characterized by Mullerian duct anomalies. The characteristic triad of this syndrome includes didelphys uterus, obstructed hemivagina, and ipsilateral renal agenesis (hence, also known as Obstructed Hemivagina and Ipsilateral Renal Agenesis or OHVIRA syndrome). The clinical presentation of HWW is nonspecific and patients may present with abdominal/pelvic pain, dyspareunia, or dysmenorrhea. However, the imaging findings of HWW are characteristic and discussed in this case report of a 16-year-old female who presented with abdominal pain and dyspareunia. Keywords: Herlyn-Werner-Wunderlich syndrome, Obstructed Hemivagina and Ipsilateral Renal Agenesis syndrome, Dyspareunia, Magnetic Resonance Imaging