Neuro-Behçet – Clinical and radiological findings in a Patient of Sub-saharan African origin

Abstract

Behçet's disease is a rare, systemic variable vessel vasculitis mostly seen in patients from the Middle East, Northern Africa and Central Asia. Neuro-Behçet disease (NBD) is often diagnosed in patients with known Behçet's disease who present with neurological symptoms and radiological features of central nervous system involvement. There are very few cases with neuro-Behçet reported from Sub-Saharan Africa in the literature. We report a case of severe parenchymal neuro-Behçet with pseudo-tumoral brainstem lesions in a young male patient of South African origin.

Keywords

• Neuro-Behçet disease
• Sub-Saharan Africa
• Waterfall sign
• Cascade sign
• Pseudo-tumors