Novel transcatheter treatment for staged closure of Abernethy malformation with portal hypoplasia

Abstract

Portosystemic shunts are rare congenital malformations that come to attention due to various hepatic and extrahepatic manifestations. Management of this malformation is dictated by the presence and adequacy of intrahepatic portal radicals. Staged occlusion of the shunt is recommended in patients with severely hypoplastic portal radicals. We describe a novel transcatheter technique that we improvised for staged occlusion of Abernethy malformation in a 2-year-old girl.

Keywords

• fenestrated device
• portosystemic shunt
• pulmonary hypertension