Bilateral Sturge–Weber Syndrome With Glaucoma: A Rare Presentation

Abstract

Sturge–Weber syndrome (SWS) or encephalotrigeminal angiomatosis is a rare congenital and dermatological disorder. It is one of the phakomatoses and is associated with unilateral port-wine stain of the face, ipsilateral glaucoma, seizures, mental retardation, and ipsilateral leptomeningeal angioma. However, different variants have been described. We describe the case of a 13-year-old female patient with bilateral SWS associated with advanced glaucoma in both the eyes and absent neurological involvement. Surgical treatment with Ahmed glaucoma valve was performed in both the eyes at an interval of 2 weeks for achieving a lower level of intraocular pressure.

Keywords

• Ahmed glaucoma valve
• bilateral Sturge–Weber syndrome
• glaucoma