Indian Journal of Paediatric Dermatology (Jan 2020)

Keratosis follicularis spinulosa decalvans: A dermoscopic perspective

  • Sudharani Chintagunta,
  • Priyanka Jaju

DOI
https://doi.org/10.4103/ijpd.IJPD_133_19
Journal volume & issue
Vol. 21, no. 2
pp. 138 – 141

Abstract

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Keratosis follicularis spinulosa decalvans (KFSD) is a rare follicular disorder characterized by widespread keratosis pilaris and progressive scarring alopecia of the scalp, eyebrows, and axillae. This condition is sometimes associated with photophobia and keratoderma. This is X-linked genodermatoses predominantly seen in males. It is unusual in females as they are carriers or have milder symptoms. Here, we report a dermoscopic perspective of this rare presentation of KFSD in an 11-year-old female.

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