Contemporary Clinical Dentistry (Jan 2019)

Oral manifestations of Nance–Horan syndrome: A report of a rare case

  • Neil De Souza,
  • Paul Chalakkal,
  • Sergio Martires,
  • Renita Soares

DOI
https://doi.org/10.4103/ccd.ccd_490_18
Journal volume & issue
Vol. 10, no. 1
pp. 174 – 177

Abstract

Read online

Nance–Horan syndrome (NHS) or X-linked cataract dental syndrome is an extremely rare condition affecting multiple systems. It is characterized by ophthalmological, dental, and facial anomalies. Individuals display facial dysmorphism, mandibular prognathism, congenital cataract, and strabismus. Common dental findings include notching of incisors, supernumerary teeth, and mulberry molars. This article aims to provide an update on NHS while reporting previously unreported findings such as talon's cusp and taurodontism.

Keywords