Journal of Pediatric Surgery Case Reports (Jul 2020)
Undifferentiated duodenal sarcoma with rhabdoid features
Abstract
Tumors of the pediatric gastrointestinal tract are uncommon, with duodenal malignancies being extremely rare. Malignant rhabdoid tumor is a rare highly aggressive tumor that occurs in young children with a very poor clinical outcome. The tumor is characterized by a diffuse proliferation of “rhabdoid cells,” which are round or polygonal with eccentric nuclei, prominent nucleoli, and glassy eosinophilic cytoplasm containing hyaline-like inclusion bodies. Very few cases of malignant tumors with rhabdoid features of the gastrointestinal tract are described in literature, but probably none so far in the duodenum of a pediatric patient. We present a case of a eleven year old with an undifferentiated tumour of the duodenum with rhabdoid features on histopathology, who underwent multimodality management and is doing well at 1 year of follow up.