Journal of Pediatric Surgery Case Reports (Jul 2020)

Undifferentiated duodenal sarcoma with rhabdoid features

  • Parag J. Karkera,
  • Pradnya S. Bendre

Journal volume & issue
Vol. 58

Abstract

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Tumors of the pediatric gastrointestinal tract are uncommon, with duodenal malignancies being extremely rare. Malignant rhabdoid tumor is a rare highly aggressive tumor that occurs in young children with a very poor clinical outcome. The tumor is characterized by a diffuse proliferation of “rhabdoid cells,” which are round or polygonal with eccentric nuclei, prominent nucleoli, and glassy eosinophilic cytoplasm containing hyaline-like inclusion bodies. Very few cases of malignant tumors with rhabdoid features of the gastrointestinal tract are described in literature, but probably none so far in the duodenum of a pediatric patient. We present a case of a eleven year old with an undifferentiated tumour of the duodenum with rhabdoid features on histopathology, who underwent multimodality management and is doing well at 1 year of follow up.

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