Annals of Pediatric Cardiology (Jan 2022)

Pulmonary artery aneurysm: Harbinger of an ominous disease

  • Deepanjan Bhattacharya,
  • Deepa Sasikumar,
  • Ayyappan Anoop,
  • Jineesh Valakada,
  • Nitin Naik,
  • Baiju Sasi Dharan

DOI
https://doi.org/10.4103/apc.apc_49_21
Journal volume & issue
Vol. 15, no. 1
pp. 77 – 79

Abstract

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An 11-year-old girl presented with chronic cough and recurrent hemoptysis. On examination, she had features of right heart failure and cyanosis, with severe pulmonary hypertension on echocardiogram. Computed tomography pulmonary angiography showed aneurysmal dilatations of the pulmonary artery with elevated erythrocyte sedimentation rate and C-reactive protein and positive human leukocyte antigen B51. A diagnosis of Hughes–Stovin syndrome (vascular variant of Behcet's syndrome) was confirmed, and she was started on immunosuppression, on which there was improvement.

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