Frontiers in Dentistry (Apr 2014)

Clinical Management of Glanzmann's Thrombasthenia: A Case Report.

  • Indu Varkey,
  • Kavita Rai,
  • Amitha M Hegde,
  • Mangalpady Shenoy Vijaya,
  • Vinod Idicula Oommen

Journal volume & issue
Vol. 11, no. 2

Abstract

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Glanzmann's thrombasthenia (GT) is a rare, genetically inherited platelet disorder in which the platelet glycoprotein IIb/IIIa (GP IIb/IIIa) complex is either deficient or, dysfunctional. The incidence is about 1 in 1,000,000. This case report deals with a 4 year-old girl diagnosed with GT presenting with dental caries and periapical lesions in the primary mandibular first molars. To provide the best care, an interdisciplinary approach was followed by a team consisting of pediatric dentists, pediatricians and anesthesiologists. Complete oral rehabilitation was planned under general anesthesia which included extractions, multiple esthetic restorations and space maintainers with the utmost care to prevent unwarranted bleeding.

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