PARRY-ROMBERG SYNDROME

Abstract

Introduction: the progressive hemifacial atrophy or Parry-Romberg syndrome is a rare disease, of slow clinical evolution that generates atrophy of the soft tissues. It compromises frequently only one side of the face, where the left side is the most affected. The disease usually establishes in early ages and with the time it could compromise one or more branches of the trigeminal nerve. In this occasion, a case in which the diagnosis was notoriously late, despite repeated consultation due to facial asymmetry and other manifestations, is presented. Case record: a 73-year-old-female patient from a Colombian rural area, who attended several times to consultation due to facial asymmetry without obtaining a definitive diagnosis is presented. She had clinical history of orbito-zygomatic and right shoulder trauma two decades ago. Also, clinical history of two ophthalmological surgeries: Cataract and glaucoma. It was observed a notorious depression in the right cheek with marked signs of atrophy, accompanied of periodic migraine disorders and local symptoms. And a skin biopsy of the cutaneous adnexal, where the atrophy was observed, was taken. There were not demonstrated other neurological lesions. Conclusions: the Parry-Romberg syndrome is a chronic disease that could have ophthalmological or neurological implications. It involves migraine symptoms, paresthesias and facial asymmetry that merits early diagnosis and adequate treatment, so much of the progressive as stationary phase. Rev.cienc.biomed. 2015;6(1):142- 149 KEYWORDS Facial asymmetry; Facial hemiatrophy; Vasculitis.

Keywords

• Facial asymmetry; Facial hemiatrophy; Vasculitis