Erythrokeratodermia variabilis and erythrokeratoderma en cocardes: Case series with review of literature

Abstract

Erythrokeratodermia variabilis (EKV) are a rare heterogeneous group of inherited cornification disorders. They are characterized by two distinct morphological types of skin lesions: Fixed hyperkeratotic plaques and sharply marginated, pruritic, and migratory erythematous lesions. We report three cases of EKV along with a review of literature.

Keywords

• En cocardes
• erythrokeratodermia variabilis
• hyperkeratotic plaque
• migratory erythema