JLUMHS (Jun 2018)

Recurrent Rapenzul Syndrome in a Male Child; A Rare Surgical Entity

  • Nand Lal Kella ,
  • Mumtaz Ahmed Qureshi,
  • Imtiaz Ahmed Qureshi

DOI
https://doi.org/10.22442/jlumhs.181720560
Journal volume & issue
Vol. 17, no. 02
pp. 106 – 108

Abstract

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Rapunzel syndrome is a rare entity when the undigested tuft of hairs accumulated in the stomach and extends beyond the pylorus in the small intestine with a presentation of vomiting, pain in epigastrium and a palpable mass. Recurrence of this pathology is extremely rare, and upto now, only six cases have been reported. We report a male who was partially deaf and dumb, presented with trichophagia and trichobezoar in the age of 5 and 9 years. Both times gastrostomy was performed and trichobezoars were removed completely which were extending in the small intestine. Post-operative recovery was un-eventful and the patient has been referred to the psychiatrist for further management.

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