Nuss Procedure for pectus excavatum repair in a patient with osteogenesis imperfecta

Abstract

A 17-year-old male with Osteogenesis Imperfecta (OI) type 1 and history of prior spinal instrumentation for kyphosis presented with severe symptomatic pectus excavatum (PEx). His Haller index was 6.7 with a Pectus Correction Index of 51%. He underwent uncomplicated Nuss procedure with insertion of 3 bars and complete repair of the PEx. A single sternal fracture was sustained during correction and healed without deformity. After two years, he developed left-sided pain and two of 3 bars were removed with maintained chest correction. This case report demonstrates the feasibility of Nuss procedure in adolescents with OI and outlines improvements to the technique in future patients with OI.

Keywords

• Osteogenesis imperfecta
• Pectus excavatum
• Nuss
• MIRPE