Emergency thoracic endovascular aortic repair with celiac artery coverage in hereditary hemorrhagic telangiectasia

Abstract

Celiac artery (CA) coverage during thoracic endovascular aortic repair has been demonstrated to be a feasible and effective strategy for selected cases. However, there is a potential risk of ischemic complications due to CA coverage in patients with certain types of hereditary hemorrhagic telangiectasia (HHT). Herein, we report a case of thoracoabdominal aortic rupture in a patient with HHT that was successfully treated with emergency thoracic endovascular aortic repair covering the CA preceded by hepatic artery bypass. We also review the hepatic circulatory derangements and unique considerations in the surgical management of HHT.