Extranodal NK/T-cell lymphoma, nasal type, primarily involving ovary

Abstract

Extranodal NK/T-cell lymphoma, nasal type (ENKTL) is a rare disease in the Western countries. Cases involving extranasal sites often have poorer prognosis than nasal cases.We report a patient with an extranodal NK/T[HYPHEN]cell lymphoma of nasal[HYPHEN]type, in the right ovary. She had surgical removement of the involved ovary and was treated with CEOP[HYPHEN]B based therapy followed by high[HYPHEN]dose therapy with autologous stem cell support. She remains in complete remission six years after diagnosis. Stage I ENKTL in the ovary is an unusual manifestation, and to our knowledge not described earlier.