Cicatricial ectropion correction for a case of amniotic band syndrome

Abstract

Background: Amniotic band syndrome (ABS) or amniotic deformity, adhesions and mutilations (” ADAM” ) is a spectrum of rare congenital malformations related to an early phase of organogenesis. In the craniofacial region, ABS could manifest in several forms. A rare form of ABS with Tessier Cleft-9 associated with atypical Cleft-2 presenting with a cicatricial ectropion is reported and management of the condition is discussed. Key Points: ABS causing oro-facial deformities is increasingly being reported. Surgical management requires staged correction and is often challenging. As growth is dynamic, evolving problems should be anticipated. Frequent follow-up and early intervention could prevent unfavourable complications. Main Lessons Learnt: ABS has craniofacial components and it requires an adequate understanding of principles of growth and healing to plan corrective surgeries for such complicated and rare conditions.

Keywords

• amniotic band syndrome
• amniotic deformity
• adhesions and mutilations
• cicatricial ectropion
• tessier cleft-9