Ectopic Ureter Causing Hydrometra in a Case of Cervical Dysgenesis with Vaginal Agenesis

Abstract

Cervical agenesis or dysgenesis is the defect of vertical fusion of the mullerian duct and the urogenital sinus. The reported incidence is 0.01% in general population. Up to 53% of patients with mullerian agenesis have concomitant congenital malformations and hence these patients should be thoroughly evaluated for the same. We report a case of cervical dysgenesis with ectopically located right ureter in the uterus. This patient had cervical obstruction with absent vagina. Conservative surgical approach was adopted. Cervical reconstruction with cervicovaginal anastomosis with the neovagina was done. The ectopically located ureter was cut and reimplanted into the bladder. Hence in patients with cervical agenesis or dysgenesis radicle approach like hysterectomy should be adopted only in case of failure of conservative surgery. Thus giving the patient a chance for healthy reproductive life and prevent premature ovarian failure.

Keywords

• cervicovaginal anastomosis
• neocervix
• neovagina