Journal of Indian Academy of Oral Medicine and Radiology (Jan 2007)
Ewing′s Sarcoma of the Ramus of Mandible - Report of a Case
Abstract
Ewing′s Sarcoma is a highly lethal round cell sarcoma of unknown etiology that was first described by ′James Ewing′ in 1921. Ewing′s sarcoma is one of the most aggressive bone tumors known and accounts for 4-7% of primary bone malignancies. It tends to affect the long bones; nearly 50% of the reported cases have occurred in the femur or pelvic bones. Only 2-7% of cases involve the maxillofacial region, usually involving the mandible ramus, and a few reported cases have involved the maxilla. Ewing′s sarcoma usually develops during the first two decades of life, and affects males twice as often as females. Approximately 90% of reported cases occurring in the mandible have been primary lesions, and 10% have been metastasis. Here, we report a case of Ewing′s sarcoma occurring primarily in the mandibular ramus of a 18 year old male patient with emphasis on histopathological findings and imaging.