A Case of Multisystemic Langerhans Cell Histiocytosis in an Adult

Abstract

A 23-year-old female smoker presented in late 2008 with a large left pneumothorax. She had multiple spontaneous pneumothoraces in 2007 which required pleurectomy. A presumptive diagnosis of lymphangioleiomyomatosis (LAM) was made in 2007 after the high-resolution computed tomography (HRCT) of the thorax revealed bilateral interlobular septal thickening and multiple thin walled cystic air spaces without lobar predilection, and with preservation of lung volumes.

Keywords

• multisystemic langerhans cell histiocytosis
• lymphangioleiomyomatosis