Klippel–Trenaunay syndrome with arterio-veno-lymphatic malformation: A rare presentation

Abstract

Klippel–Trenaunay syndrome (KTS) is a rare disorder characterized by triad of vascular malformations, varicose veins, and bony or soft tissue hypertrophy involving an extremity. Port wine stain is the most common vascular malformation associated with this syndrome. Various other rare vascular malformations described are angiokeratomas, angiokeratoma circumscriptum naeviformae, angiodermatitis, etc. This is the first instance, to the best of our knowledge, describing the capillary, venous, and lymphatic malformations in a same case of KTS.

Keywords

• klippel–trenaunay syndrome
• lymphangioma circumscriptum
• multiple angiokeratomas
• port wine stain