Retinoblastoma in Late Childhood

Abstract

Retinoblastoma, the commonest intra-ocular tumor of childhood, is rare after the age of 5 years. We report a case of retinoblastoma in a 10 year-old boy, who presented with a fungating proptosed tender mass involving the entire left eye and the orbit. A clinical diagnosis of retinoblastoma was made. Exenteration of the left orbit was done. Histopathology revealed well-differentiated retinoblastoma with the involvement of optic nerve section. CSF and bone marrow aspirates did not show any malignant cells. This paper highlights the delayed presentation of retinoblastoma in late childhood and discusses the treatment modalities of orbital retinoblastoma. Though retinoblastoma in late childhood is uncommon, it should be considered in the differential diagnosis of leukocoria and a fungating proptosed mass. Key Words: Retinoblastoma, late childhood, fungating proptosed mass.