Case Reports in Surgery (Jan 2017)

Successful Outcome and Biliary Drainage in an Infant with Concurrent Alpha-1-Antitrypsin Deficiency and Biliary Atresia

  • Andrew W. Wang,
  • Kimberly Newton,
  • Karen Kling

DOI
https://doi.org/10.1155/2017/9348461
Journal volume & issue
Vol. 2017

Abstract

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We describe the rare instance of concomitant biliary atresia and alpha-1-antitrypsin deficiency and the first documented successful portoenterostomy in this scenario. The potential for dual pathology must be recognized and underscores that prompt diagnosis of biliary atresia, despite concomitant alpha-1-antitrypsin deficiency, is essential to afford potential longstanding native liver function.