Medical Journal of Dr. D.Y. Patil University (Jan 2014)

Dyke-Davidoff-Masson syndrome: A case report

  • Biswajyoti Rath,
  • Maheswar Samant,
  • Kali P Swain,
  • Ashok K Mallick

DOI
https://doi.org/10.4103/0975-2870.140494
Journal volume & issue
Vol. 7, no. 5
pp. 672 – 674

Abstract

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Dyke-Davidoff-Masson Syndrome (DDMS), also called as cerebral hemiatrophy, is a rare clinical condition characterized by seizures, facial asymmetry, contralateral spastic hemiplegia or hemiparesis, with learning difficulties. It is commonly diagnosed in presence of associated radiologic findings, which include cerebral hemiatrophy with homolateral hypertrophy of the skull and sinuses. We present a 21-year female with increased frequency of convulsion and abnormal behavior for the last 2 months. She had a known seizure disorder for 15 years and had mental subnormality. On physical examination, she was disoriented with mild right hemiparesis. On CT scan the brain showed unilateral left cerebral atrophy.

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