Frontiers in Immunology (Dec 2020)
Prenatal Diagnosis for Primary Immunodeficiency Disorders—An Overview of the Indian Scenario
- Reetika Malik Yadav,
- Maya Gupta,
- Aparna Dalvi,
- Umair Ahmed Bargir,
- Gouri Hule,
- Snehal Shabrish,
- Jahnavi Aluri,
- Manasi Kulkarni,
- Priyanka Kambli,
- Ramya Uppuluri,
- Suresh Seshadri,
- Sujatha Jagadeesh,
- Beena Suresh,
- Jayarekha Raja,
- Prasad Taur,
- Sivasankar Malaischamy,
- Priyanka Ghosh,
- Shweta Mahalingam,
- Priya Kadam,
- Harsha Prasada Lashkari,
- Parag Tamhankar,
- Vasundhara Tamhankar,
- Shilpa Mithbawkar,
- Sagar Bhattad,
- Prerna Jhawar,
- Adinarayan Makam,
- Vandana Bansal,
- Malathi Prasad,
- Geeta Govindaraj,
- Beena Guhan,
- Karthik Bharadwaj Tallapaka,
- Mukesh Desai,
- Revathi Raj,
- Manisha Rajan Madkaikar
Affiliations
- Reetika Malik Yadav
- Center of Excellence for PIDs, Department of Pediatric Immunology and Leucocyte Biology, ICMR-National Institute of Immunohaematology, Mumbai, India
- Maya Gupta
- Center of Excellence for PIDs, Department of Pediatric Immunology and Leucocyte Biology, ICMR-National Institute of Immunohaematology, Mumbai, India
- Aparna Dalvi
- Center of Excellence for PIDs, Department of Pediatric Immunology and Leucocyte Biology, ICMR-National Institute of Immunohaematology, Mumbai, India
- Umair Ahmed Bargir
- Center of Excellence for PIDs, Department of Pediatric Immunology and Leucocyte Biology, ICMR-National Institute of Immunohaematology, Mumbai, India
- Gouri Hule
- Center of Excellence for PIDs, Department of Pediatric Immunology and Leucocyte Biology, ICMR-National Institute of Immunohaematology, Mumbai, India
- Snehal Shabrish
- Center of Excellence for PIDs, Department of Pediatric Immunology and Leucocyte Biology, ICMR-National Institute of Immunohaematology, Mumbai, India
- Jahnavi Aluri
- Center of Excellence for PIDs, Department of Pediatric Immunology and Leucocyte Biology, ICMR-National Institute of Immunohaematology, Mumbai, India
- Manasi Kulkarni
- Center of Excellence for PIDs, Department of Pediatric Immunology and Leucocyte Biology, ICMR-National Institute of Immunohaematology, Mumbai, India
- Priyanka Kambli
- Center of Excellence for PIDs, Department of Pediatric Immunology and Leucocyte Biology, ICMR-National Institute of Immunohaematology, Mumbai, India
- Ramya Uppuluri
- Department of Pediatric Hematology-Oncology, Blood Marrow Transplantation, Apollo Hospitals, Chennai, India
- Suresh Seshadri
- Department of Clinical Genetics & Genetic Counseling, Mediscan Systems, Chennai, India
- Sujatha Jagadeesh
- Department of Clinical Genetics & Genetic Counseling, Mediscan Systems, Chennai, India
- Beena Suresh
- Department of Clinical Genetics & Genetic Counseling, Mediscan Systems, Chennai, India
- Jayarekha Raja
- Department of Clinical Genetics & Genetic Counseling, Mediscan Systems, Chennai, India
- Prasad Taur
- Department of Immunology and Department of Pediatric Hemato-Oncology, Bai Jerbai Wadia Hospital for Children, Mumbai, India
- Sivasankar Malaischamy
- MedGenome Labs Private Limited, Bangalore, India
- Priyanka Ghosh
- MedGenome Labs Private Limited, Bangalore, India
- Shweta Mahalingam
- MedGenome Labs Private Limited, Bangalore, India
- Priya Kadam
- MedGenome Labs Private Limited, Bangalore, India
- Harsha Prasada Lashkari
- Department of Pediatrics, Kasturba Medical College Hospital, Manipal Academy of Higher Education, Mangalore, India
- Parag Tamhankar
- Centre for Medical Genetics, Mumbai, India
- Vasundhara Tamhankar
- Centre for Medical Genetics, Mumbai, India
- Shilpa Mithbawkar
- Centre for Medical Genetics, Mumbai, India
- Sagar Bhattad
- Division of Pediatric Immunology and Rheumatology, Department of Pediatrics, Aster CMI Hospital, Bangalore, India
- Prerna Jhawar
- Department of Fetal Medicine, Motherhood Hospital, Bangalore, India
- Adinarayan Makam
- 0Department of Fetal Medicine, Adi Advanced Centre for Fetal Care, Bangalore, India
- Vandana Bansal
- 1Fetal Medicine Department Surya Hospitals, Mumbai, India
- Malathi Prasad
- 2Fetal Medicine Centre, Trichy, India
- Geeta Govindaraj
- 3Department of Pediatrics, Government Medical College, Kozhikode, Calicut, India
- Beena Guhan
- 3Department of Pediatrics, Government Medical College, Kozhikode, Calicut, India
- Karthik Bharadwaj Tallapaka
- 4CSIR-Centre for Cellular and Molecular Biology (CSIR-CCMB), Hyderabad, India
- Mukesh Desai
- Department of Immunology and Department of Pediatric Hemato-Oncology, Bai Jerbai Wadia Hospital for Children, Mumbai, India
- Revathi Raj
- Department of Pediatric Hematology-Oncology, Blood Marrow Transplantation, Apollo Hospitals, Chennai, India
- Manisha Rajan Madkaikar
- Center of Excellence for PIDs, Department of Pediatric Immunology and Leucocyte Biology, ICMR-National Institute of Immunohaematology, Mumbai, India
- DOI
- https://doi.org/10.3389/fimmu.2020.612316
- Journal volume & issue
-
Vol. 11
Abstract
Prenatal Diagnosis (PND) forms an important part of primary preventive management for families having a child affected with primary immunodeficiency. Although individually sparse, collectively this group of genetic disorders represents a significant burden of disease. This paper discusses the prenatal services available for affected families at various centers across the country and the challenges and ethical considerations associated with genetic counseling. Mutation detection in the index case and analysis of chorionic villous sampling or amniocentesis remain the preferred procedures for PND and phenotypic analysis of cordocentesis sample is reserved for families with well-characterized index case seeking PND in the latter part of the second trimester of pregnancy. A total of 112 families were provided PND services in the last decade and the presence of an affected fetus was confirmed in 32 families. Post-test genetic counseling enabled the affected families to make an informed decision about the current pregnancy.
Keywords
- prenatal diagnosis
- chorionic villus sampling
- maternal contamination
- cordocentesis
- flow cytometry
- variants of unknown significance