Congenital Radial Dysplasia

Abstract

Radial dysplasia (RD) is a congenital condition which can affect the entire upper limb, compromising multiple tissues, and it always features alterations in the thumb. It can be uni- or bilateral condition, the latter being very disabling. Treatment with manipulations, casts and/or orthoses is recommended for the least severe presentations of this disease. The surgical treatment is reserved for the most severe cases, and carpal centralization is the treatment of choice today. The most frequent complication of this intervention is the recurrence of the deformity. The patients submitted to the surgical treatment report a significant improvement in the cosmetic aspect of the extremity. The current challenge is to improve the follow-up and the use of functional assessment tools regarding the results.

Keywords

• radial dysplasia
• congenital upper limb anomalies
• congenital hand surgery