A rare combination of anomalous origin of right pulmonary artery from the ascending aorta with congenital tricuspid valve anomaly and severe tricuspid regurgitation

Abstract

Anomalous origin of a pulmonary artery (PA) from the aorta is a rare presentation in adulthood. As these patients invariably develop severe pulmonary hypertension in infancy itself, prognosis is poor. Here, we present a patient with anomalous origin of right PA from the aorta and congenital tricuspid valve anomaly with severe tricuspid regurgitation, a very rare combination surviving to adult life.

Keywords

• anomalous pulmonary artery
• congenital heart disease
• hemitruncus
• pulmonary hypertension
• tricuspid valve disease