Type one segmental Darier′s disease

Abstract

A 50-year-old woman presented with multiple pruritic hyperpigmented papules in a zosteriform pattern involving the abdomen and back on the left side and in a linear pattern involving the left arm and forearm of 2 years duration. Histopathology revealed striking suprabasal acantholysis and marked dyskeratosis in the form of corps ronds and grains, a picture consistent with Darier′s disease (DD). Type one segmental DD involving multiple sites in zosteriform and linear patterns is an uncommon condition and is reported for its rarity.

Keywords

• Darier′s disease (DD)
• linear
• segmental
• unilateral
• zosteriform