Anais Brasileiros de Dermatologia (Mar 2020)

Complete form of pachydermoperiostosis,

  • Mônica Larissa Padilha Honório,
  • Guilherme Holanda Bezerra,
  • Vivianne Lira da Câmara Costa

DOI
https://doi.org/10.1016/j.abd.2019.04.009
Journal volume & issue
Vol. 95, no. 1
pp. 98 – 101

Abstract

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Abstract Pachydermoperiostosis (PDP) or primary hypertrophic osteoarthropathy (PHO) is a rare hereditary disease characterized by digital clubbing, pachydermia, and periostosis. Its pathogenesis is uncertain and the diagnosis is based on clinical and radiological data. A complete form of the syndrome is reported in a male patient with disease onset in adolescence, with compatible clinical and radiological findings, presenting the three cardinal findings as well as other associated manifestations, such as hyperhidrosis and acne.

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