Enchondromatosis with cervical spine involvement in children: small series and review

Abstract

Objective: to present different variants of the clinical course and surgical treatment of an extremely rare vertebral pathology – enchondromatosis with involvement of the cervical vertebrae in children. Two cases of local and multiple forms of bone dyschondroplasia with damage to the cervical vertebrae, accompanied by orthopedic and neurological complications in children aged 7 and 11, are described. As a result of the operation, complaints were completely stopped in one child and neurological disorders were eliminated in another. The diagnosis was verified histologically. The results were followed up for more than 2 years and 1 year after the operation, respectively. Present-day data on Ollie’s disease in children are presented. Indications, timing and volume of surgical intervention for bone dyschondroplasia are determined individually, depending on the size, location, and number of enchondromas. However, if the cervical spine involvement is complicated by increasing pain and neurological disorders, it is precisely decompression of the spinal cord that should be set as a priority aim of the surgery.

Keywords

• ollie’s disease
• multiple bone chondromatosis
• dyschondroplasia
• children
• spinal deformity
• spinal cord compression