Indian Journal of Ophthalmology (Jan 2008)

Extranodal <i>Rosai-Dorfman Disease</i> presenting as an isolated epibulbar mass

  • Maheshwari Rajat,
  • Shekde Satish

Journal volume & issue
Vol. 56, no. 6
pp. 502 – 504

Abstract

Read online

Rosai-Dorfman disease is a rare idiopathic disorder characterized by painless lymphadenopathy with cervical involvement in more than 80% cases. We report a case of Rosai-Dorfman disease presenting as an isolated epibulbar mass in a healthy young adult male. Epibulbar involvement in Rosai-Dorfman disease is a rare presentation as can be seen from a review of all literature. The presentation, differential diagnosis and treatment are discussed.

Keywords