Postpartum fevers, a rare presentation of secondary hemophagocytic lymphohistiocytosis

Abstract

Abstract Hemophagocytic lymphohistiocytosis (HLH) is a rare disease of excessive immune system activation. We report a case of HLH in a 20‐year‐old primigravid woman who presented with postpartum fevers. She was successfully treated with dexamethasone and anakinra, a deviation from the HLH‐94 protocol, to preserve her ability to breastfeed.

Keywords

• anakinra
• fever of unknown origin
• hemophagocytic lymphohistiocytosis
• postpartum fevers